Sjogren’s syndrome related sensory motor neuropathy and autonomic neuropathy: A Case report

Authors

  • Amtul Farheen Lebanon VA medical center
  • William Jens Pennstate Hershey Medical Center
  • Cunfeng Pu Pennstate Hershey Medical Center
  • Aiesha Ahmed Pennstate Hershey Medical Center

DOI:

https://doi.org/10.17161/rrnmf.v1i5.14526

Keywords:

sjogrens, neuropathy, NCS, EMG, biopsy

Abstract

Neurologic involvement has been reported in primary Sjogren’s syndrome (SS) in approximately 10–25% of cases 1, 2, 3. Peripheral neuropathy is a major neurological manifestation of Sjögren's syndrome 4 and its etiology has been considered to be vasculitis in the peripheral nerves 2. While neuropathic symptoms of SS can be varied, it is unusual to have two different types of neuropathic presentations simultaneously in a patient. We describe a case of Sjogren’s syndrome presenting with autonomic symptoms who was noted to have large fiber neuropathy on EMG and inflammatory changes on nerve biopsy.

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Author Biographies

William Jens, Pennstate Hershey Medical Center

Clinical Assisstant Professor of Neurology

 

Aiesha Ahmed, Pennstate Hershey Medical Center

Associate Professor of Neurology

References

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Published

2020-11-30

How to Cite

Farheen, A., Jens, W., Pu, C., & Ahmed, A. (2020). Sjogren’s syndrome related sensory motor neuropathy and autonomic neuropathy: A Case report. RRNMF Neuromuscular Journal, 1(5), 25–28. https://doi.org/10.17161/rrnmf.v1i5.14526

Issue

Section

Clinic Stuff (Case Reports)