“Ear of the Lynx" radiological sign in a patient with Primary Lateral Sclerosis.


  • Nakul Katyal MD University of missouri
  • Praveen D. Attele DO University of Missouri-Columbia
  • Bryce C. Hoelscher MD University of Missouri-Columbia
  • Erik R. Ensrud MD University of Missouri-Columbia
  • Richard J. Barohn MD University of Missouri-Columbia




Ear of the Lynx, Hereditary Spastic Paraplegia, Primary Lateral Sclerosis


The “Ear of the Lynx" radiological sign refers to fluid attenuated inversion recovery (FLAIR) sequence cone-shaped abnormalities at the forceps minor region of genu of corpus callosum, seen on magnetic resonance imaging (MRI) of the brain. This radiological sign has been reported in Hereditary Spastic Paraplegia (SPG) type 11 and SPG Type 15. In this case report, we discuss the first description of this radiological sign in a 59 year old female patient with PLS.



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How to Cite

Katyal, N., Attele, P. ., Hoelscher, B., Ensrud, E., & Barohn, R. (2022). “Ear of the Lynx" radiological sign in a patient with Primary Lateral Sclerosis . RRNMF Neuromuscular Journal, 3(3), 32–35. https://doi.org/10.17161/rrnmf.v3i3.18049



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